Also known as the port wine stain or naevus flammeus, this tumour tends to be distributed over the area supplied by one or more of the branches of the fifth cranial nerve and usually remains throughout life as a dark red discolouration in the skin (Figure 15.5). The importance of this particular appearance is its association with secondary glaucoma and hae-mangioma of the meninges. The latter produces calcification and a characteristic X-ray appearance. The combination of lesions is known as the Sturge-Weber syndrome. There can be hypertrophy of the affected area of the face, leading to asymmetry.
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